- published: 12 Aug 2015
- views: 401610
Cystic fibrosis (CF) is a genetic disorder that affects mostly the lungs but also the pancreas, liver, kidneys, and intestine. Long-term issues include difficulty breathing and coughing up mucus as a result of frequent lung infections. Other signs and symptoms include sinus infections, poor growth, fatty stool, clubbing of the fingers and toes, and infertility in males among others. Different people may have different degrees of symptoms.
CF is inherited in an autosomal recessive manner. It is caused by the presence of mutations in both copies of the gene for the cystic fibrosis transmembrane conductance regulator (CFTR) protein. Those with a single working copy are carriers and otherwise mostly normal. CFTR is involved in production of sweat, digestive fluids, and mucus. When CFTR is not functional, secretions which are usually thin instead become thick. The condition is diagnosed by a sweat test and genetic testing. Screening of infants at birth takes place in some areas of the world.
Actors: Einar Kuusk (producer), Danielle Rayne (actress), Peter A.T. McQuillan (producer), Vincent Conti (director), Vincent Conti (producer), Vincent Conti (writer), James Gerardi (actor), James Gerardi (actor), Michael Segovia (actor), Michael Segovia (actor), Justin Benoit (composer), Tamara Inaebnit (actress),
Genres: Sci-Fi, Short,Actors: Brendan Butler (miscellaneous crew), Nardeep Khurmi (actor), Christina Broccolini (actress), Mark A. Keeton (actor), Aaron C. Peer (actor), Adriano Valentini (director), Adriano Valentini (writer), Adriano Valentini (editor), Adriano Valentini (producer), Daniel Pfeffer (producer), Christopher Costa (miscellaneous crew), Alexa Kahn (actress), Michael Mazzeo (actor), Carmine DiBenedetto (actor), Dane C. Reiley (producer),
Plot: Bartender Gabe Garibaldi is the King of the Clubscene in Montreal - the nightlife capital of North America. His uncle's popular club - Club Touch - is the hottest spot in the city. Every night, Gabe and his buddies - club promoter Paul DelDuca and celebrity DJ Vinni V - create the wild unforgettable atmosphere for the Montreal locale and tourists from all over the world. Gabe lives a high profile lifestyle. The girls love him. The guys want to be him. He gets what he wants when he wants it. And he loves it. Until he meets a girl who calls him out on his shallow lifestyle. She doesn't fall head over heals for him. She doesn't care that he's best friends with DJ Vinni V. She's unlike any girl he's ever met. He realizes his life of perpetual hedonism is leaving him unfulfilled and disconnected. But he's unsure how to get out, how to change.
Keywords: drunkenness, forgotten, garibaldi, hook-up, moment-of-truth, montréal-quebec-canada, text, touchActors: Lambert Wilson (actor), Steven Mackintosh (actor), Thure Lindhardt (actor), Antoine Chappey (actor), Marianne Faithfull (actress), Mark Gilvary (actor), Johnny Melville (actor), Jens Albinus (actor), Chris Wyatt (editor), Daniel O'Meara (actor), Lucy Russell (actress), C.S. Leigh (director), C.S. Leigh (writer), C.S. Leigh (producer), Gwenaëlle Simon (actress),
Genres: Drama,Actors: J.C. Brandy (miscellaneous crew), J.C. Brandy (actress), Jennifer S. Deayton (miscellaneous crew), Paul Heiman (editor), Ernesto Godoy (actor), Forest Wise (director), Forest Wise (actor), Forest Wise (producer), Forest Wise (writer), George Ferris (actor), Zoë Nathenson (actress), Laura Calcaterra (miscellaneous crew), Mark Stansbury (actor), Mike Dytri (actor), Mike Dytri (producer),
Genres: ,China's Final Port - Mega Structure. Yangshan Port (Chinese: 洋山港, p Yángshān Gǎng), formally the Yangshan Deep-Water Port (洋山深水港, p Yángshān Shēnshuǐ Gǎng), is a deep water port for container ships in Hangzhou Bay south of Shanghai. Connected to Shanghai's Pudong New Area by the Donghai Bridge and forming part of the Port of Shanghai, the islands of Greater and Lesser Yangshan are administered separately as part of Zhejiang's Shengsi County. Read More: https://en.wikipedia.org/wiki/Yangshan_Port
Platinum Games' finest shooter has come to PC and it's simply immense. Here's how the game looks and runs on PC, and how it compares to the PlayStation 3 version. Subscribe to Digital Foundry: http://bit.ly/DFSubscribe Support the DF Patreon and download an ultra-pristine version of this video: https://www.digitalfoundry.net/2017-05-25-vanquish-pc-the-port-youve-been-waiting-for
Link to my Twitter: https://twitter.com/VinylicPuma Hey guys, back with another Youtube Video and today I wanted to make a video on a rereleased game for the PC called Vanquish. Vanquish is a Third Person Shooter that's a fusion of games like Gears of War and Bayonetta with crazy bullet time and fast movement. For this specific video, I figured I would go over some of what I think are the best guns and weapons to use and or upgrade in Vanquish. As always, if you liked this video leave a like and let me know what you think!
This video shows insertion of the Bard Powerport, but the technique is the same for most ports
Here's a step by step process for accessing and de-accessing a port. This is a monthly flush, but we also put a sterile dressing on for the purpose of showing how we have found the best way to have a smooth application of the dressing. We take time to show you the proper way to stay sterile, and little tips and tricks we have learned during the ten years that I have been independent with my port care. Watch "Packing My Hospital Bag" → https://youtu.be/jjT5Jsf9Y-s HOSPITAL ROOM TOUR → https://youtu.be/QR9SpJW6WY0 Subscribe to our channel → http://goo.gl/LvdRdF → We post new vlogs everyday showing daily life with Cystic Fibrosis! FOLLOW US ON SOCIAL MEDIA Mary's Instagram → http://instagram.com/freyliving Twitter → http://twitter.com/thefreylife Google+ → http://google.com/+thefreylife ...
Visit our Online Store → http://thefreylife.com/store Watch Yesterday's Vlog → https://youtu.be/CpDJBHTFqB0 ONE YEAR AGO → https://youtu.be/jfbSensO614 2 Years Ago → https://youtu.be/Mu0ReI_isNg ↓↓↓Watch more from The Frey Life↓↓↓ What is Cystic Fibrosis → https://youtu.be/llrxGuU5o5c New Here Playlist → https://goo.gl/EZgra7 Draw My Life → https://youtu.be/jHYw-gQimws Service Dog Q&A; → https://youtu.be/5Nh1fS1N9NQ Cystic Fibrosis Q&A; → https://youtu.be/YDJ3yIS6SWI Are We Having Kids? → https://youtu.be/uHjEcXvn2ZU Peter's Channel → https://youtube.com/peterfreylife Subscribe to our channel → http://goo.gl/LvdRdF → We post new vlogs everyday showing daily life with Cystic Fibrosis! Help us make these videos more accessible by contributing closed captions! → http://www.youtube.com/time...
Si quieres donar, hazlo aquí! https://youtube.streamlabs.com/UC4o7PkjtWNW1yD0IwldI9kA Compra aquí barato y apoya al canal!! https://www.g2a.com/r/srserpiente Recuerda usar el código de descuento SERPS para usar un 3% menos! --------------- Gofres sideriales en la descripción ------------------ Ahora y de nuevo en Twitch! http://www.twitch.tv/srserpiente Follow me in twittá: https://twitter.com/SrSerpiente1 Sigueme en el MENTOR de steam y no te pierdas nada! http://steamcommunity.com/groups/SrSerpienteOficial#curation O también puedes en facebook: https://www.facebook.com/SrSerpienteOficial Hoy en el canal ¿Que uso? Capturadora: Elgato Hd60: http://e.lga.to/SrSerpiente Ordenador: Procesador: Intel I7 6770k http://amzn.to/YF9Lqi Gráfica: Gigabyte Nvida GForce Gtx 1070 FTW Ram: 2 8Gb ddr3...
For more video and news as it breaks, head to http://afl.com.au
Top 10 biggest shipping ports in the world. Checkout practical maritime eBooks at http://www.marineinsight.com/guides
California women's swimwear brand Beach Riot teams up with brand boutique, Port of Long Beach to bring you a co branded one piece bathing suit for this summer. The suit features a blend of modern and classic with it's backless low cut and one piece functionality. Color options for the project suit are a black with white Port branding along with an heather grey and white logo. These are in limited quantity and only available exclusively in store and online at Port along with the Beach Riot website. Models Amanda Booth and Xian Mikol Video by Paul Liddle @ StadiumLA.com
http://passportal.com.au/ CALLUM PAUL'S PINK HEATH & BUBBLER BOY DECKS AVAILABLE WORLDWIDE NOW USA | PERMANENT DISTRIBUTION | sales@permanentdist.com UNITED KINGDOM | KEEN DISTRIBUTION | mike@keendist.co.uk JAPAN | FTC TOKYO DISTRIBUTION | yuske@ftcjapan.com NORWAY | GO~SKATE DISTRIBUTION | emil@goskate.no DENMARK/SWEDEN/FINLAND | DIVISION DISTRIBUTION | sean@divisiondistr.com FRANCE/GERMANY/BENELUX | CONTINENTAL DISTRIBUTION | contact@continentaldist.com SOUTH KOREA | RVVSM DISTRIBUTION | taehyun@rvvsm.com
"Boat turns toward the port" taken from the upcoming mini-album "Narrow" by Soap&Skin; Released Feb 13th in Europe and March 19th in UK/Ireland
I wanna dance with you this whole night
I hope the music never slows up
I hope this place don't never close up
Hold tight
'cause you're the only one who feels right
Girl I know it's now or never
I wanna dance with you forever
So hold on tight - never let me go, baby
'cause I can feel the rhythm of your love
And when you get yourself in motion
Girl it's tearin' my emotions right in two
Hold tight
And we will dance into the moonlight
All the stars they will surround us
We will be so glad we found us
So hold on tight - never let me go, baby
'cause I can feel the rhythm of your love
And when you get yourself in motion
I get lovin' notions all for you - yes I do
Hold tight
And we will dance into the moonlight
I hope the music never slows up